Cystic fibrosis is a lung condition that inhibits breathing. This condition can also cause other serious health problems, including digestive issues and organ damage.
Cystic fibrosis is associated with severe effects, and many people with the disorder have a shortened lifespan. However, the right treatment can effectively relieve symptoms and greatly improve a person’s quality of life.
Cystic fibrosis results from dysfunction in cells responsible for producing fluids, including sweat, mucus, and fluids used for digestion. A genetic mutation causes the normally thin fluid to become thicker, which impedes breathing and contributes to other health issues.
Parents pass the gene that causes cystic fibrosis on to their children. In order for symptoms to develop, both parents must pass on the mutated gene. People who have family members with cystic fibrosis are encouraged to undergo genetic testing to determine their risk of passing along the gene to their children.
While there is no cure for cystic fibrosis, certain medications can have a positive impact on the disease. Accordingly, doctors may prescribe:
Doctors can also prescribe a class of drugs that act upon a dysfunctional protein that causes fluids in the body to thicken. By improving the function of this protein, lung function can also improve.
Doctors can combine drug regimens with other therapies. For instance, many people with cystic fibrosis experience relief with pulmonary rehabilitation, airway clearing techniques, and surgical procedures, such as those to remove the nasal polyps that often accompany the disorder.